pemphigus paranéoplasique et myasthénie, associés à un sarcome inflammatoire folliculaire ... Réponse au rituximab
Posté : 18 juil. 2016 11:09
Lu sur http://onlinelibrary.wiley.com/doi/10.1 ... avedsearch
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Paraneoplastic pemphigus and myasthenia gravis, associated with inflammatory pseudotumor-like follicular dendritic cell sarcoma: response to rituximab
Lifang Wang, Hui Deng* andMei Mao Version of Record online: 15 JUL 2016
DOI: 10.1002/ccr3.625
Key Clinical Message
Paraneoplastic pemphigus (PNP) is an autoimmune blistering disease associated with neoplasms. The disease is most commonly of lymphoproliferative origin and presents high mortality. We describe a patient with PNP and myasthenia gravis associated with inflammatory pseudotumor-like follicular dendritic cell sarcoma, as well as the response to rituximab.